Glomangiopericytoma, three cases in nine days; case reports and Brief review

Authors

  • M. Patrick Stagg MD* Baton Rouge General Internal Medicine Residency Program, Baton Rouge, LA, 70809, USA https://orcid.org/0000-0002-5818-0601
  • Henry P.Barham MD Rhinology and Skull Base Research Group, Baton Rouge General Medical Center, Baton Rouge, LA, USA ,Sinus and Nasal Specialist of Louisiana, Baton Rouge, Louisiana, USA
  • Rahul V. Ramaraju Department of Chemical Engineering, Louisiana State University, Baton Rouge, LA, 70803, USA
  • Sai Samyuktha Bandaru MD Baton Rouge General Internal Medicine Residency Program, Baton Rouge, LA, 70809, USA https://orcid.org/0000-0001-5466-2809
  • Mohamed A. Taha MD Sinus and Nasal Specialist of Louisiana, Baton Rouge, Louisiana, USA, Department of Otorhinolaryngology, Faculty of Medicine, Cairo University, Cairo, Egypt
  • Sanjay Juneja MD Baton Rouge General Internal Medicine Residency Program, Baton Rouge, LA, 70809, USA

DOI:

https://doi.org/10.52845/JORR/2022/3.1.1

Abstract

Glomangiopericytoma is a rare sinonasal tumor. We report three cases of this rare disease that presented in nine days to one subspecialty practice. Histochemical and DNA sequencing confirmed the diagnosis in each case. Endoscopic sinonasal surgery provided complete resection in each case. The occurrence of three cases to one practice within a 2-week timeframe may suggest GPC is under-recognized. Routine sequencing to detect CTNNB1 mutations and staining for smooth muscle actin of suspicious sinonasal tumors may increase the frequency of GPC detection.

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Published

2022-01-04

How to Cite

M. Patrick Stagg MD*, Henry P.Barham MD, Rahul V. Ramaraju, Sai Samyuktha Bandaru MD, Mohamed A. Taha MD, & Sanjay Juneja MD. (2022). Glomangiopericytoma, three cases in nine days; case reports and Brief review. Journal of Otolaryngology and Rhinology Research , 3(01), 65–69. https://doi.org/10.52845/JORR/2022/3.1.1

Issue

Vol. 3 No. 01 (2022): Journal of Otolaryngology and Rhinology Research

Section

Case Reports